Backgroud: Retinal racemose hemangioma (RRH) is a rare congenital disorder that often co-occurs with other\nocular complications. In this study, we present a case of RRH complicated with retinal vein obstruction in three\nbranches and provide a review of ocular complications and associations with RRH.\nCase presentation: One case of RRH is presented. Fundus examination, fluorescein angiography (FFA) and optical\ncoherence tomography (OCT) of the patient identified Group 3 RRH complicated with retinal vein occlusions in the\nsuperotemporal, inferotemporal, and inferonasal branches. Macular edema, which causes visual impairment, was\ndetected. A brief literature review was also presented. The PubMed database was searched for RRH or related\nkeywords to find reports of ocular complications or associations published on or before Dec. 31, 2013. A total of\n140 papers describing167 RRH cases were found. The mean age of diagnosis was 22.97 years. Ocular complications\nwere mentioned in 32 (19.16%) cases. Retinal vein occlusion (46.88%) was the major ocular complication in RRH,\nfollowed by hemorrhage (34.38%). Eight (4.79%) cases were associated with other ocular diseases such as\nSturgeââ?¬â??Weber syndrome , Morning glory disc anomaly and macroaneurysm.\nConclusions: Although RRH is a relatively non-progressive condition, its complications may lead to vision loss and\nshould be treated in time.
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