Theductus venosus serves as an important vascular pathway for intrauterine circulation. This case presents a description of an absent\nductus venosus in a female patient with Noonan syndrome, including both prenatal and postnatal imaging of the anomaly. In the\nsetting of the anomalous vascular connection, the umbilical vein courses inferiorly to the iliac vein in parallel configuration with\nthe umbilical artery. This finding was suspected based on prenatal imaging and the case was brought to attention when placement\nof an umbilical catheter was thought to be malpositioned given its appearance on radiography. Ultrasound imaging confirmed the\nanomalous course. This is in keeping with prior descriptions in the literature of an association between Noonan syndrome and\naberrant umbilical venous drainage. This case illustrates the need for awareness of this condition by the radiologist, allowing for\nidentification on radiographs and the recommendation for further confirmatory imaging. Further, the case illustrates the value\nof paying particular attention to the fetal course of the umbilical vessels in patients with suspected Noonan syndrome, as this\npopulation is particularly at risk for anomalous vasculature.
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